Prenatal diagnosis of the hurler syndrome: Report on 40 pregnancies at risk

In 40 pregnancies at risk for the Hurler syndrome 13 affected fetuses were detected by the demonstration of an α-L -iduronidase deficiency and an increased level of ³⁵S-sulphate incorporation. The diagnoses were confirmed by the analysis of fetal tissues and/or cultured fetal skin fibroblasts. Microassays for α-L -iduronidase, using phenyl α-L -iduronide and more recently 4–methyl-umbelliferyl α-L -iduronide, enabled a reliable diagnosis to be made within 15 to 18 days after amniocentesis. ³⁵S-sulphate incorporation has been a valuable adjunct in cases with a low (heterozygote) enzyme activity.     

社会主义荣辱观的意义与启示

本文对胡锦涛总书记提出的“八荣八耻”社会主义荣辱观的重大现实意义与启示全面进行了论述，并从内在联系上阐明了社会主义荣辱观八个方面的辩证统一，论证了践行社会主义荣辱观，实质上是实现党的宗旨、保持党的先进性的迫切需要。     

ERP管理专业计算机课程在多媒体教学中的应用

ERP计算机课程往往可有效利用多媒体技术进行教学.ERP管理专业计算机课程在多媒体教学中如何应用显得尤为重要.通过采用多种教学形式、充分应用多媒体教学、灵活运用多媒体课件来促进ERP管理专业的计算机课程在多媒体教学的发展.     

Water pricing towards sustainability of water resources: a case study in Beijing

The role of water pricing for managing water resources is widely recognized in many areas of the world because of the increasing scarcity of water resources, a high competition between water uses and environmental degradation. Based on the analysis of cost of water, this paper explores which types of cost should be reflected in the water pricing enhancing the sustainability of water resources. The principle of full cost pricing in which the cost should include supply cost, opportunity cost and externalities is proposed as a means to achieve the sustainability of water resources. In a case study of Beijing, low water price is analyzed as one reason for unsustainable water consumption. Thus water pricing justified is necessary and pressing. It is proposed to justify water price in phased manner and eventually towards full cost pricing. The assessment of impacts on water resources by raising water price shows water pricing could alleviate the conflict between water supply and demand. This paper concludes that water pricing can play an effective role in enhancing the sustainability of water resources in Beijing.     

加油站油气回收处理技术的研究及应用进展

介绍了国内外加油站油气回收处理技术现状及应用进展，阐明了国内开发的重点应是：密封加油系统及设备、吸收式油气回收装置及分散吸附集中处理系统。