First-trimester prenatal diagnosis of Sanfilippo C disease

At 10 weeks' gestation, chorionic villus biopsy was obtained from a woman at risk for Sanfilippo type C disease. Acetyl-CoA: α-glucosaminide N-acetyltransferase activity was markedly deficient. The pregnancy was terminated at 12 weeks' gestation and follow-up study on fetal fibroblasts confirmed the diagnosis.     

Carbon isotope ratios in logged and unlogged boreal forests: Examination of the potential for determining wildlife habitat use

Due to assimilation of recycled CO₂ from litter decomposition and photosynthetic changes in carbon fractionation at low light levels, the foliage at the base of a forest is often more depleted in¹³C compared to that exposed to the atmosphere in either the canopy or in open clearings. This is referred to as the canopy effect. African research has indicated that these habitat differences in foliar ¹³C can be substantial enough to affect the carbon isotope ratios of resident fauna. Previous work documenting a 30-year chronology on moose teeth from Isle Royale National Park indicated a progressive depletion in¹³C and suggested that this could be due to forest regrowth following extensive burning. The present study examined the assumption implicit in this hypothesis that foliar ¹³C varies between open and closed boreal forest sites. I found a marginal canopy effect of 2 ¹³C difference between upper canopy and ground flora for a forest in northwestern Ontario and an average difference of 1.2 in under- and mid-story vegetation between closed forests and open clear-cuts. Because of these small differences, the utility of carbon isotope analysis in quantifying temporally integrated exploitation of deforested habitats will be low for northern boreal locations. In denser forests, such as those in the tropics or western North American where the canopy effect can be expected to be much greater, ¹³C analysis may still offer some promise for determining selection by wildlife of disturbed habitats.     

Characterisation of Organic Matter and Carbon Cycling in Rehabilitated Lignite-rich Mine Soils

Open-cast lignite mining in the Lusatian mining district resulted in rehabilitated mine soils containing up to four organic matter types: (1) recent plant litter, (2) lignite deposited by mining activity, (3) carbonaceous ash particles deposited during amelioration of the lignite-containing parent substrate and (4) airborne carbonaceous particles deposited during contamination. The influence of lignite-derived carbon types on the organic matter development and their role in the soil carbon cycle was unknown. This paper presents the findings obtained during a six year project concerning the impact of lignite on soil organic matter composition and the biogeochemical functioning of the ecosystem. The organic matter development after rehabilitation was followed in a chronosequence of rehabilitated mine soils afforested in 1966, 1981 and 1987. A differentiation of the organic matter types and an evaluation of their role within the ecosystem was achieved by the use of ¹⁴C activity measurements, ¹³C CPMAS NMR spectroscopy and wet chemical analysis of plant litter compounds. The results showed that the amount and degree of decomposition of the recent organic matter derived from plant material of the 30 year old mine soil was similar to natural uncontaminated forest soil which suggests complete rehabilitation of the ecosystem. The decomposition and humification processes were not influenced by the presence of lignite. On the other hand it was shown that lignite, which was thought to be recalcitrant because of its chemical structure, was part of the carbon cycle in these soils. This demonstrates the need to elucidate further the stabilisation mechanisms of organic matter in soils.     

真,假草本咖啡种子的鉴别

在对草本咖啡（Ｃａｓｓｉａｓｏｐｎｅｒａｉｉｎｎ）、望江南（ＣａｓｓｉｓｏｃｃｉｄｅｎｔａｌｉｏＬ．）和决明（ＣａｓｓｉａｔｏｒａＬ．）种子的大小、颜色、形态进行了观察、研究，并对其形态特征进行了解剖学的分析后，提出了鉴别３种种子的方法。     

青藏铁路救援指挥系统的研究

通过对青藏铁路特点及运营模式的分析,提出构建青藏铁路事故救援指挥系统的重要性。结合青藏铁路信息化总体规划,在充分利用青藏铁路各信息系统及通讯网络基础上,利用地理信息系统(GIS)技术和无线通讯技术,建设具有指挥、控制、通信及情报(C3I)功能的青藏铁路事故救援指挥系统。提出了系统应达到的目标功能,结合青藏铁路生产作业实际情况,给出了系统实现的信息流程、体系结构,并开发了原型系统。系统将青藏铁路多源信息整合并结合GIS技术以直观的电子地图、图像等方式展示出来,实现了救援预案管理和智能化查询、匹配;并通过应急无线通讯设备实现事故现场视频、图像实时播放及指挥调度与事故现场间的语音双向通讯;同时可建立事故数据库,为统计报告和事故分析服务。     

基于C/S与B/S混合模式的大气污染监测系统设计

以C／S与B／S混合模式为基础的大气监测系统、既能充分发挥网络资源的便捷化，实现企业监测数据与管理系统的快速链接，又充分利用C／S模式的安全性能，以保证系统的安全性。因而此系统是当前的一种较新型的，功能较为强大的网络监测系统。     

飞行目标自动跟踪系统设计综述

主要介绍了GPS技术的最新发展、应用及原理，结合成熟的GPS技术，设计了一套对飞行目标的位置自动跟踪系统。该系统以C51系列单片机为数据处理核心器件，前接GPS接收机，将GPS的测量信息进行分析处理，产生控制信号，输出给后续的伺服机构，驱动伺服机构完成自动跟踪。本系统可以在森林防火指挥系统中，完成火灾监测、人员、物资调配等工作，使火灾造成的损失降低到最小。     

利用单片机实现对云台的转动控制

以单片机为核心，将单片机的串口通过RS-485与云台相连，采用RS-485总线标准，通过PELCO—P协议，在C51环境中编制程序，实现了对(多台)云台的方位转动控制。     

Knowledge, values, uses and management of the Araucaria araucana forest by the indigenous Mapuche Pewenche people: A basis for collaborative natural resource management in southern Chile

One of the most important endemic tree species of Chile and at the same time one of the most endangered ones is Araucaria araucana (Mol.) C. Koch, the monkey‐puzzle tree. It grows in the Andes Mountains, homeland of the indigenous Mapuche Pewenche people who depend on this tree. This paper is based on field research that investigated the ecological knowledge, uses and management of the Araucaria araucana forest by indigenous Mapuche Pewenche people based on the socio‐cultural, spiritual and ecological relationships they have with the Araucaria forest, to find out how indigenous people and their knowledge could contribute to sustainable Araucaria forest management. A Mapuche Pewenche community located in the IX region of Chile contributed to this study. Based on the analyses this paper illustrates the nature of indigenous ecological knowledge of Araucaria araucana on the one hand, and its utility in native forest management on the other. The research shows that the Mapuche Pewenche hold ecological knowledge and conduct practices to manage their Araucaria forest in a balanced way. They conserve and use forest biodiversity at one and the same time. This paper provides recommendations for sustainable Araucaria forest management and conservation strategies ex‐situ and in‐situ incorporating indigenous knowledge and scientific knowledge and for promoting a collaborative natural resources management.     

Discounting in the presence of scarce ecosystem services

The discount rate for cost-benefit analysis has to take account of future scarcity of ecosystem services in consumption and production. Previous literature focuses on the first aspect and shows the importance of the relative price effect, for given growth rates of consumption and ecosystem services. This paper focuses on intermediate ecosystem services in production and shows that for limited substitutability and a low growth rate of these ecosystem services, the growth rate of consumption, and thus the discount rate, declines towards a low value. Using a Ramsey growth model, the paper distinguishes three cases. If ecosystem services can be easily substituted, the discount rate converges to the usual value in the long term. Secondly, if ecosystem services can be easily substituted in production but not in consumption, the relative price effect is important. Finally, and most interestingly, if ecosystem services cannot be easily substituted in production, the discount rate declines towards a low value and the relative price effect is less important. Another part of the previous literature has shown that a declining discount rate is the result of introducing several forms of uncertainty, but this paper reaches that conclusion from an endogenous effect on the growth rate of the economy.