First-trimester prenatal diagnosis of aspartylglucosaminuria

Fetal aspartylglucosaminuria (AGU) was studied during the first trimester of pregnancy in six at-risk pregnancies using chorionic villus samples. The activity of aspartylglucosaminidase (AGA) was high in five cases, indicating an unaffected fetus. This was confirmed through delivery of healthy newborns with a normal pattern of urinary oligosaccharides. Low enzyme activity in an uncultured biopsy specimen and in cultured amniotic fluid cells in one case demonstrated that the fetus was affected. The pregnancy was terminated and the prenatal diagnosis was confirmed by showing reduced AGA activity in cultured fibroblasts of the fetus.     

公害民事责任三论

当今，公害已成为公众十分关注的社会问题之一。为维护我国公民的合法权益，我国环境保护法律体系中，对公害造成的社会性危害作了具体规定，文章对民事责任基本从三方面作了比较系统完整的探讨。公害民事责任的法律规定。公害民事责任的特点，公害民事责任与资源破坏民事责任的关系，在公害民事责任与一般民事责任关系的分析中，阐述了追公害民事责任的法律依据和公害民事责任是一种特殊的侵权的民事责任的特性。     

Opportunities and constraints for Product-oriented Environmental Management Systems (P-EMS)

Product-oriented Environmental Management Systems (P-EMS) are a logical extension of current, often primarily process- of facility-oriented Environmental Management Systems. The Dutch government promotes P-EMS as part of its product-oriented environmental policies. The idea of P-EMS is to enable producers to make environmentally responsible decisions on product development and product strategies, in collaboration with suppliers and customers. This paper summarises example P-EMS projects in The Netherlands for two segments of industry, namely retail and manufacturing industry. Moreover two other initiatives will be covered that deal with the development of tools to facilitate P-EMS in two other industry sectors (food processing and building). Success factors that emerge from these initial experiences are: focus on partners that have a strong incentive to act, application of screening Life Cycle Assessments (LCA) or user-shells for LCA, and focus on improvements that can be implemented on the short term.     

浅谈如何做好“十一五”环境统计工作

环境统计工作存在的问题：指标体系设置不合理、数据时效性差、数据质量不高、统计人员流动性大，采取的措施：精简完善指标体系、规范工作程序和审核办法、抓好统计范围、污染源监测及数据核查提高数据质量、加强统计队伍建设等。     

直流输电线路对环境影响探究

随着科学技术的发展,许多领域在提高工效、节约资源、降低能耗和保护环境方面得到很大的提高.在国内直流输电线路应用就是之一.本文回顾了直流输电线路这项技术发展史,分析了该项技术在技术上和经济上等方面的优缺点,以及直流输电线路对环境和人的影响因素,通过实际工程估算结果说明了直流输电线路的环境影响,为今后开展该项工作提供借鉴.     

生命周期评价数据库分析与建模

基于关系数据库和面向对象程序设计理论建立了生命周期评价数据库系统。通过综合分析生命周期评价数据，根据生命周期评价数据的数据类型，将数据分为产品评价数据、产品档案数据、基础材料数据和影响评价基础数据，相应的设计了4个数据库。运用关系数据库理论分别对4个数据库建立了物理结构模型。     

改进灰色系统模型在城市噪声预测中的应用

把城市噪声作为一个灰色系统,分别通过GM(1,1)模型和改进灰色系统模型GM'(1,1),对城市噪声进行预测,并进行精度检验.改进的灰色系统模型GM'(1,1)在精度上均优于GM(1,1)模型,但是GM'(1,1)在计算上比较复杂,需要通过计算机迭代来实现.     

固相微萃取-毛细管气相色谱法测定水中有机污染物

固相微萃取是一种快速、简便、集萃取浓缩于一体的样品前处理技术,具有分析快速、灵敏度高、无需有机溶剂的优点。用固相微萃取-毛细管气相色谱分析水中甲醇、丙酮、异丙醇、乙醇、乙腈、丙烯腈,检出限可达0.003～0.03mg/L。     

建立上海市突发环境事件应急防范和处置体系的研究

随着人类活动的加剧和工业的不断发展，全球突发环境事件日渐频繁。因此，在日常工作中应加强突发环境事件的应急防范和反应体系建设。防患于未然。文章概述了国内外对突发环境事件的防范及应急处置现状，分析了突发环境事件的特点和危害，简要阐述了建立上海市突发环境事件应急处置指挥系统的重要性及必要性，重点介绍了上海市突发环境事件的应急指挥、应急响应及灾害评估体系，并介绍了与突发环境事件应急处置有关的几个问题。以增加系统的可操作性。同时。提出了加强上海市应急防范和处置系统建设的对策及建议。     

A review of EMAS in Greece: is it effective?

EMAS certification is a common practice among the European companies. However, based on the data from the Greek Ministry of Environment, only 10 companies were EMAS certified in Greece by December 2003. The aim of this study is to identify and summarize the experiences of the EMAS certified companies that operate in Greece. Based on the results of the study, the major advantage from the EMAS implementation seems to be the closer monitoring of the production process while the main cost item is the infrastructure upgrading.