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Prenatal rupture of a left ventricular diverticulum: a case report and review of the literature
Authors:A Bernasconi  A L Delezoide  F Menez  E Vuillard  J F Oury  A Azancot
Institution:1. Perinatal cardiology, Hôpital Robert Debré, Assistance Publique Hôpitaux de Paris, Paris, France;2. Fetal pathology, Hôpital Robert Debré, Assistance Publique Hôpitaux de Paris, Paris, France;3. Obstetric and Gynecology, Hôpital Robert Debré, Assistance Publique Hôpitaux de Paris, Paris, France
Abstract:Congenital left ventricular diverticulum is a rare malformation. We report a case of a ruptured congenital left ventricular diverticulum in a 24-week-old fetus. The fetus was referred for a large and circumferential pericardial effusion confirmed by cross-sectional echocardiography in our tertiary fetal cardiology unit. Pericardiocentesis removed 25 mL of old hematic fluid. The fetus died 5 days later. The pathological examination showed a ruptured submitral fibrous diverticulum of the posterior wall of the left ventricle. There is no previous report in the literature of prenatal rupture of a cardiac diverticulum. The submitral location and the fibrous wall of the diverticulum is uncommon. As regards this case, we reviewed the diagnostic criteria and the outcome of 11 cases of prenatal cardiac diverticulum reported in the literature. Copyright © 2004 John Wiley & Sons, Ltd.
Keywords:prenatal diagnosis  submitral diverticulum  pericardial effusion  prenatal rupture
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